Reddy, 2007: Overview of all reported HSP-SPAST patients

Index patient Sex Ethnicity Country of origin AAO AAE Family history Symptoms Initial symptoms Reported mutations
No
n.a.
USA
25
51
n.a.
Babinski sign
-Pure or uncomplicated
Spasticity, lower limb
Spastic gait
Walking aids
Hyperreflexia in upper limbs
Lower limb muscle weakness
Show more (+4)
n.a.
Yes
n.a.
USA
24
48
n.a.
Spasticity, lower limb
-Pure or uncomplicated
Hyperreflexia in upper limbs
Lower limb muscle weakness
Spastic gait
Babinski sign
Show more (+3)
n.a.
No
n.a.
USA
3
23
n.a.
Lower limb muscle weakness
Babinski sign
Hyperreflexia in upper limbs
Spastic gait
Spasticity, lower limb
-Pure or uncomplicated
Show more (+3)
n.a.